Guenther Schneider1, Alexander Massmann2, Peter Fries2, Marcus Katoh2, Urban Geisthoff3, Arno Buecker2
1University Hospital of Saarland, Homburg / Saar, Germany; 2University Hospital of Saarland, Germany; 3Clinics of City of Cologne/Holweide, Germany
Hereditary hemorrhagic telangiectasia (HHT), also known as Rendu-Osler-Weber disease, is an autosomal-dominant inherited vascular disorder associated with mucocutaneous, pulmonary, cerebral and visceral arteriovenous malformations (AVM). Pulmonary arteriovenous shunts (PAVM) are associated with high morbidity and mortality. The primary choice of treatment of PAVMs is catheter embolization with platinum coils, which is technically safe and effective. However, even in an initial successful occlusion, there may be a reperfusion of embolized feeding vessels or opening of collateral vessels. This study shows that contrast-enhanced magnetic resonance angiography (CE-MRA) is a useful tool for follow-up examinations of treated PAVMs, in which platinum coils were used for embolization, preferable to CT and even global pulmonary catheter angiography.