Meeting Banner
Abstract #0574

7T MRI Reveals Abnormal Iron Deposition and Microstructure in Premanifest and Manifest Huntington’s Disease

Jingwen Yao1, Melanie A. Morrison1,2, Angela Jakary1, Sivakami Avadiappan1, Julia Glueck3, Theresa Driscoll3, Michael Geschwind3, Alexandra Nelson3, Duan Xu1,2, Christopher P. Hess1,3, and Janine M. Lupo1,2
1Department of Radiology and Biomedical Imaging, University of California, San Francisco, San Francisco, CA, United States, 2UCSF/UCB Graduate Program in Bioengineering, University of California, San Francisco, San Francisco, CA, United States, 3Department of Neurology, University of California, San Francisco, San Francisco, CA, United States

Synopsis

Keywords: Neurodegeneration, Neurodegeneration, Huntington's disease, Movement disorderWe used QSM and DTI at 7T to investigate iron dysregulation and microstructure disruption in subcortical regions in Huntington’s disease (HD). We observed significant volume loss and increased iron deposition in the striatum and globus pallidus, and increased FA in the striatum. The deep cerebellar nuclei (dentate nuclei) showed a unique transient increase in volume and susceptibility in premanifest patients, implicating it as a new marker of HD disease progression that is sensitive to the pre-symptomatic window of HD. We also found varying relationships between imaging features in different brain regions, warranting further analyses of subregional changes.

How to access this content:

For one year after publication, abstracts and videos are only open to registrants of this annual meeting. Registrants should use their existing login information. Non-registrant access can be purchased via the ISMRM E-Library.

After one year, current ISMRM & ISMRT members get free access to both the abstracts and videos. Non-members and non-registrants must purchase access via the ISMRM E-Library.

After two years, the meeting proceedings (abstracts) are opened to the public and require no login information. Videos remain behind password for access by members, registrants and E-Library customers.

Click here for more information on becoming a member.

Keywords