Restrictive cardiomyopathy (RCM) is a rare form of heart muscle disease that is characterized by restrictive ventricular filling. The overall prognosis of RCM is poor with progression to heart failure and mortality. The primary aim of this study is to evaluate the association between myocardial strain and major RCM adverse events, such as death. The secondary aim is to assess the difference of MRI variables in RCM between women and men. The results demonstrated that decreased left-atrial longitudinal strain is significantly associated with mortality in RCM, independent of other MRI and clinical measures and beyond the need for gadolinium administration.